That visceral pain differs significantly from other types of pains has been appreciated by clinicians for centuries. As recently as the turn of this century, however, investigators were in disagreement about the source(s) of visceral pain. Lennander (24) and MacKenzie (28) maintained that pain was not derived directly from a viscus (see discussion in ref. (25)), whereas others provided evidence for what they called ``true visceral pain'' or ``splanchnic pain'' ((43); discussion in ref. (25)). The issue is no longer contentious, but its consideration emphasizes several points important to our current understanding of visceral pain. First, pain per se does not arise from all viscera (e.g., liver parenchyma), but pain associated with such viscera does arise when the capsule containing that viscus distends or becomes inflamed. Second, tissue injury (or threat of such injury) may not be required or necessary for production of visceral pain, as it is for pain from cutaneous structures (see refs. (6) and (37) for discussion). Thus, unlike cutaneous pain, the adequate stimuli for production of visceral sensation, including pain, are not yet fully appreciated.
Chapter 7 Table 1: Characteristics
of visceral pain
| Referral/transferral to cutaneous structures |
| Diffuse and difficult to localize |
| Enhanced autonomic and/or motor reflexes |
| Cutaneous and deep tissue hyperalgesia |
Chapter 7 Table 2: Naturally
occurring visceral stimuli
| Hollow organ distention |
| Ischemia |
| Inflammation |
| Muscle spasm |
| Traction |
The first investigators to employ controlled, constant pressure stimuli in studies of sensation from the gut were apparently Lipkin and Sleisinger (26). Using balloons to distend the esophagus, ileum, or colon, they documented that the latency from the onset of the stimulus to patient reports of pain was directly related to the intensity of the distending stimulus. At lesser distending pressures, they found that the stimulus was not reported by subjects as painful for up to 1 min after the onset of distention and was preceded by the sensation of pressure over large abdominal or thoracic areas. They determined in their studies that the minimal intraluminal pressures to produce painful sensations from the esophagus, ileum, and colon were 39 to 47, 44 to 59, and 40 to 50 mm Hg, respectively. A more complete description of such studies is available elsewhere (37). With respect to distention of hollow organs, Lewis (25) commented earlier that distention of the gut was most painful when long, continuous segments of the gut were simultaneously distended. Even greater pressures within smaller segments of the gut were not as efficacious in producing painful sensations. Thus, spatial summation is clearly an important contributor to visceral pain mechanisms.
Inflammation or ischemia of a viscus generally leads to altered sensations from the viscus, including pain. The example of Wolf's patient Tom is instructive (49). When Tom's stomach mucosa was ``normal,'' neither pinching a fold of mucosa with a forceps nor electrical stimulation of the mucosa, applied at an intensity sufficient to cause ``intense pain in the tongue,'' was painful. However, after the mucosa was rendered ``red, boggy and edematous'' by application of powdered mustard after removal of the mucus, intense pain occurred with application of these same stimuli to the now inflamed tissue. This should not be surprising and is in some ways analogous to the hyperalgesia associated with inflammation of cutaneous structures.
Interruption of the blood supply to most deep structures, including the viscera, also frequently leads to pain (e.g., myocardial ischemia). Experimentally, occlusion of the blood supply to the colon increases significantly the rates of spontaneous and contraction-related discharges of afferent fibers from the colon (18). Other investigators have examined the effects of ischemia/anoxia on abdominal afferents (gallbladder, pancreas, mesentery, and liver [27]) and cardiac afferents (2,4). In general, although ischemia/anoxia may reproduce a stimulus that arises naturally, occlusion of blood supply to an organ is not a stimulus generally well suited to stimulus-response experimental investigation; ischemia/anoxia is, however, a useful ``conditioning'' stimulus. Like ischemia/anoxia, inflammation also reproduces a visceral stimulus that arises naturally but is similarly associated with changes in experimental parameters only after a relatively long latency. Thus, although ischemia and inflammation are important clinically, they are better suited experimentally to condition organs and thus responses to stimuli delivered to them (e.g., mechanical distentions).
Visceral afferents terminate in the spinal dorsal horn in superficial laminae (I and IIouter ) and the neck of the dorsal horn in lamina V; visceral afferent fibers also terminate in the area around the central canal (often called lamina X). It is interesting to note that, whereas somatic afferents terminate throughout the spinal dorsal horn (i.e., laminae I-VI), cutaneous nociceptors terminate in the spinal dorsal horn in a pattern similar to visceral afferents: superficial dorsal horn and neck of the dorsal horn.
The functional classification of visceral afferents has been an issue
of some disagreement. Some visceral afferents (e.g., biliary system, colon,
ureter) have high mechanical thresholds for activation, respond only to
apparently noxious intensities of stimulation, and encode the intensity
of stimulation in this noxious range (5,18) (see
Figure 2
); these afferents are analogous to those from skin classed
as nociceptors and thus appear to subserve a similar nociceptive function
from the viscera. A greater proportion of visceral afferents, however,
have thresholds for activation in the physiological range and encode the
intensity of stimulation throughout the non-noxious and noxious ranges
of stimulation (1,21). Some of these afferents
also respond to several modalities of stimulation (e.g., mechanical, chemical)
(22) and thus may be similar to polymodal afferents
from cutaneous structures, although these visceral afferents also respond
to presumably non-noxious intensities of stimulation. Several factors likely
contribute to our present inability to classify visceral afferents (as
cutaneous afferents have been categorized; see ref. 48). First, the issue
of the adequate stimulus contributes to the problem; moreover, such stimuli
are certainly different for different organs (e.g., mechanical distention
of the colon versus ischemia of the myocardia vs inflammation of the urinary
bladder). Second, most studies have been done using only a limited array
of test stimuli because, experimentally, it is not generally an easy matter
to apply a wide range of different stimuli to often difficult-to-access
viscera. Although clinical evidence suggests that pain arising from one
viscus is similar, if not identical, to pain arising from other viscera
in terms of intensity and quality, this does not address the issues above,
but simply emphasizes that our interpretation of the sensation is consistent.
Another point to be emphasized is that the number of visceral afferents, relative to the number of afferents from cutaneous structures, is very small. The number of visceral afferents has been variously estimated to be between 2% and 10% of all afferents to the spinal cord (depending on the spinal level of input) (7,12,21). This low number is significantly out of proportion to the relative number of spinal dorsal horn neurons that respond to visceral stimulation in those same spinal segments, estimated to be 50% to 75% (10). This discrepancy is apparently explained by the significantly greater rostrocaudal spread of visceral afferent terminals in the spinal cord than the rostrocaudal spread of the more numerous cutaneous afferent terminals (46).
Further, in studies in which visceral afferents have been found by electrical stimulation, a surprising proportion have been found to not be responsive to the stimuli tested (typically mechanical). Afferents from the joint first found in this manner have been dubbed ``sleeping'' or ``silent'' afferents, awakening only after experimental inflammation of the joint (44). Similarly, irritation/inflammation of the urinary bladder has been shown to lead to increased responses to mechanical stimulation of unmyelinated pelvic nerve afferents that previously gave only weak or no responses to the same mechanical stimuli before inflammation of the bladder (16). It is now apparent that there exists a new and large group of nociceptors from somatic and visceral structures that play an important role in nociception after tissue is inflamed or injured. Accordingly, irritation/inflammation has been employed experimentally in a variety of studies to ``condition'' responses to visceral stimuli. For example, responses of spinal dorsal horn neurons to distention of the urinary bladder or noxious colorectal distention are greater after irritation of these organs with 25% turpentine (30,37). Importantly, behavioral responses of rats also are significantly influenced by prior conditioning of the colon with turpentine. For example, colorectal distention at intensities of 30 mm Hg or less produce no change in rats' behavior in a passive avoidance paradigm (i.e., these intensities are not noxious), but 30 mm Hg colorectal distention does lead to acquisition of the avoidance behavior after conditioning of the colon with turpentine (39).
As a result of increased interest and investigation into mechanisms of visceral pain, including the discovery of silent afferents and the use of conditioning stimuli that more closely approximate clinical situations, our thinking about visceral pain is undergoing rapid change. Whether there exist specific visceral nociceptors is no longer at issue, because some afferents from visceral (as well as somatic) structures have been shown to acquire new response properties, including responses to noxious stimuli, when tissue is injured or inflamed. Thus, some visceral afferents may function in all conditions to convey nociceptive information (e.g., from gallbladder or ureter), whereas afferents from other viscera undergo a change in their sensitivity to applied stimuli after irritation/inflammation of a viscus (i.e., previously silent afferents become active/responsive). In the clinical circumstance, in which irritating and/or inflammatory conditions are common, visceral nociceptors are likely active.
It should be emphasized, however, that whereas many afferents from a viscus may become active during an experimentally induced inflammation and presumably in disease (e.g., pancreatitis, malignancies), investigators are not at present able to account for the function(s) of a significant number of afferents that cannot be activated by any stimuli tested, even after irritation/inflammation of the organ. This is a recently appreciated situation, best exemplified by the work of J;auanig and colleagues (15,16). They studied unmyelinated afferent fibers innervating the pelvic viscera in cats and found that less than 10% of the afferents in the pelvic nerve could be activated by noxious mechanical distention of the urinary bladder. They also described a small number of unmyelinated afferents that were chemosensitive (mustard oil or turpentine), some of which acquired mechanosensitivity after inflammation of the bladder by these irritants. Thus, there remain a very large number of unmyelinated afferents in the pelvic nerve (perhaps as much as 90% of the total) for which no function is apparent. Extrapolating from these investigations, for which adequate stimuli were identified for a small number of afferent fibers, an obvious conclusion is that adequate stimuli have not been identified for the majority of visceral afferents in the body. Clearly, not all visceral afferents need play a role in sensation, and perhaps some of these ``unresponsive'' visceral afferents are important to other functions (e.g., monitoring gut or bladder content by sensitivity to pH, nutrients, gases, and various ions). Further, it is not to be expected that the relatively acute irritation/inflammation produced experimentally reproduces the clinical circumstance in which such insults are generally slower in onset and longer in duration. That is, it may be that more afferents are ``recruited'' into function over time as the severity of the insult progressively worsens.
Experimentally, evidence for one or more altered central mechanisms
is provided by changes in the size of receptive fields of spinal dorsal
horn neurons after some conditioning stimulus. Hylden et al. (20)
documented that inflammation of a hindpaw of the rat led to a significant
increase in the size of convergent, cutaneous receptive fields of spinal
neurons studied in dorsal horn lamina I. Also in the rat, the cutaneous
receptive fields of spinal dorsal horn neurons have been shown to increase
in size after repetitive esophageal distention (Figure
3
), repetitive gallbladder distention (8),
and repetitive colorectal distention (figure 4
).
That these convergent, cutaneous receptive fields expand in size after
repetitive distention of a viscus unquestionably implicates one or more
central mechanisms, because there is no convincing evidence for the existence
of a large number of bifurcating or dichotomizing neurons that simultaneously
innervate a cutaneous structure and a viscus. Thus, the repetitive visceral
input to the dorsal horn must alter the excitability of central neurons,
leading to several changes, including a significant increase in the size
of the receptive field from the convergent cutaneous input. Repetitive
colonic distention in humans similarly leads to an increase in the area
of referred sensation and also to a change (increase) in the reported qualities
of the stimulus (38). In these experiments, 10
consecutive distentions (60 mm Hg given 4 min apart) lead to an obvious
and significant increase in the areas of referred sensation (Figure
5A
). Comparing visual analog scale ratings during the first and last
of the 60 mm Hg distentions also reveals that the stimulus was considered
painful at the end of the series of distentions, whereas it was not uniformly
considered to be painful during the first distention (Figure
5B
). Analysis of verbal descriptors of the quality of the sensation
produced by sigmoid colon distention also revealed that subjects reported
a significant increase in the magnitude of the descriptors selected for
the sensations produced (38).
In continuing electrophysiological investigations in the rat, the convergent,
cutaneous receptive fields that increased in size after repetitive colonic
distention were found to further increase in size after conditioning of
the colon with 25% turpentine. It is interesting to note in figure
4
that the convergent, cutaneous fields, after instillation of turpentine
into the colon, grew to include the contralateral side of the rats' dorsal
body; converging, cutaneous receptive fields in untreated rats never included
an area on the contralateral body surface (36).
These results suggest that two different mechanisms may be operative, because
there appear to be two stages to the increase in size of convergent, cutaneous
receptive fields. It is possible that the receptive field would continue
to grow with repeated colorectal distention to the size finally determined
after treatment with turpentine. Results to date, however, suggest that
receptive fields increase in size during repetitive colorectal distention
over the course of 1 to 2 hr and do not increase further. Therefore, it
seems likely that an additional mechanism is engaged by the chemical insult
(e.g., recruitment of previously silent afferents from the colon and enhanced
excitability of a greater number of dorsal horn neurons than affected by
repetitive colorectal distention alone). It is understandable, on the basis
of such results, why patients' complaints of pain increase over time.
In a recent review (29), it was suggested
that a number of visceral disorders (e.g., noncardiac chest pain, nonulcer
dyspepsia, irritable bowel syndrome) may be reflections of a form of visceral
hyperalgesia and/or may involve mechanisms analogous to neuropathic conditions.
In support, there are a number of clinical observations of lowered pain
thresholds in response to distention of hollow organs (esophagus, stomach,
and colon) in some of these patients (23,41,42).
In general, these studies find that normal visceral sensations are experienced
in these patients at reduced distending pressures. It has been known for
some time, for example, that individuals with irritable bowel syndrome
have reduced thresholds to colonic distention and report a greater incidence
of pain associated with distention than do normals (42)
(Figure 6
). Further, the area of referred sensation
in normals and patients with irritable bowel syndrome clearly differ (47)
(Figure 7
). These clinical observations complement
the experimental results briefly described above, suggesting that central
mechanisms best understood in cutaneous models of hyperalgesia and central
sensitization likely also explain altered sensations from the viscera.
Central sensitization refers to alterations in the excitability of spinal
cord neurons to a variety of normal inputs following peripheral tissue
damage or irritation (50). Central sensitization
is manifest as a prolonged facilitation of reflexes and an increase in
receptive field size of dorsal horn neurons (e.g., see
Figs. 3
and
4
and ref. 50).
The central mediators involved in the development of central sensitization
are incompletely understood at present. The release of neuropeptides (e.g.,
substance P, calcitonin gene-related peptide) from the central terminals
of primary afferent fibers appears to play an important role, as does activation
of the N -methyl-d-aspartate (NMDA) receptor (11,51).
Most recently, a role for nitric oxide (NO) in NMDA-receptor-mediated facilitation
of a nociceptive reflex (33) and in the thermal
hyperalgesia produced in experimental models of hind limb inflammation
and neuropathic pain in the rat has been suggested (34;
Meller, Cummings, Traub, and Gebhart, unpublished ). NMDA receptor
activation results in an influx intracellularly of calcium that, acting
at a calmodulin site on NO synthase, leads to the production of NO (or
an NO-containing moiety) (13). NO is a small,
rapidly diffusible molecule that is believed to escape from its site of
synthesis and act as a ``retrograde'' messenger in the presynaptic terminal
or to influence activities in adjacent neurons and/or glia (see
ref. 32 for a recent review relative to NO and nociception). NO ultimately
leads to the production of cGMP, which has well-documented second messenger
functions.
The theme of visceral hyperalgesia and its ability to explain many of the clinical features of noncardiac chest pain, nonulcer dyspepsia, and irritable bowel syndrome patients is discussed in detail elsewhere (29). A further analogy considered in greater detail elsewhere (29) is that between neuropathic or sympathetically maintained pains and unknown insult to a ``visceral'' nerve. It is possible that an initiating insult, which would likely be minor and may even be missed, could produce persistent, altered sensations arising from a viscus, including pain. Campbell and colleagues have offered a unifying hypothesis to explain sympathetically maintained pain (3). They suggest that sympathetically maintained pain is a receptor disorder and that activity in cutaneous nociceptors leads to an up-regulation of adrenoceptors on the terminals of the nociceptors. If this is the case, the phentolamine test advocated by Campbell and colleagues could be useful in determination of whether a circumstance analogous to sympathetically maintained pain is associated with viscera.
There remain, however, some unresolved issues. Foremost among them is
the function of what is apparently the majority of visceral afferent fibers.
It may be that all afferents from some organs have an identified function,
but it appears that afferents from much of the viscera have no function
yet associated with them. It seems unlikely that all visceral afferents
are associated with sensation, and many may be associated with other aspects
of visceral function, including reflex functions and monitoring visceral
content. Often not considered are possible functions of visceral afferents
associated with local, trophic modulation of a viscus (31).
As investigators identify adequate stimuli for visceral afferents, appreciating
that it is likely that these adequate stimuli are different for different
viscera, our understanding of visceral sensation, and particularly visceral
pain, will improve and perhaps suggest improved treatment for pain control.